A Rare Presentation of Idiopathic Spinal Epidural Lipomatosis

*Associate Professor, ** Professor and Head, ***Resident, Institution Department of Radiodiagnosis, S. N. Medical College, Agra, U.P., India. Abstract Spinal epidural lipomatosis (SEDL) is defined as pathological overgrowth of the normal extra-dural fat and often causes dural impingement, commonly involving lumbar and thoracic spine. It is most often associated with exogenous steroid therapy and endocrinopathies like Cushing's syndrome and hypothyroidism. Idiopathic cases of SEDL in the absence of exposure to steroids or endocrinopathies is very rare; primarily seen in obese individuals. Only few cases of healthy, non-obese individuals with symptomatic epidural lipomatosis have been reported in the literature. Our case belongs to this particular group. We present a case of symptomatic epidural lipomatosis in a two-year-old, normal built boy with neck swelling and progressive weakness of limbs. Radiological and clinico-pathological features of idiopathic SEDL, along with treatment options are discussed.